Multimodality lymphatic imaging of postoperative chylothorax in an infant with Noonan syndrome: a case report
KT Pham, D Balaguru, VS Tammisetti… - European journal of …, 2020 - Springer
KT Pham, D Balaguru, VS Tammisetti, CJ Guevara, JC Rasmussen, RC Zvavanjanja…
European journal of medical research, 2020•SpringerBackground Chylothorax is a rare complication of pediatric cardiac operations that occurs
more frequently in children with Noonan syndrome, a genetic disorder associated with
cardiac defects and lymphatic anomalies. Case presentation We report a case of
postoperative chylothorax in a 6-month-old infant with Noonan syndrome where
multimodality lymphatic imaging guided management was followed. Drainage patterns of
the lymphatic capillaries in the lower and upper extremities were visualized during near …
more frequently in children with Noonan syndrome, a genetic disorder associated with
cardiac defects and lymphatic anomalies. Case presentation We report a case of
postoperative chylothorax in a 6-month-old infant with Noonan syndrome where
multimodality lymphatic imaging guided management was followed. Drainage patterns of
the lymphatic capillaries in the lower and upper extremities were visualized during near …
Background
Chylothorax is a rare complication of pediatric cardiac operations that occurs more frequently in children with Noonan syndrome, a genetic disorder associated with cardiac defects and lymphatic anomalies.
Case presentation
We report a case of postoperative chylothorax in a 6-month-old infant with Noonan syndrome where multimodality lymphatic imaging guided management was followed. Drainage patterns of the lymphatic capillaries in the lower and upper extremities were visualized during near-infrared fluorescence lymphatic imaging (NIRFLI). Dynamic magnetic resonance lymphangiography (MRL) further identified the site of leakage in the thoracic duct and subsequently guided surgical intervention.
Conclusions
Application of multimodality imaging allows for greater individualization of treatment and should be considered in patients with complex cases such as those with syndromes associated with a higher incidence of chylothorax. IRB Number: HSC-MS-13–0754, December 10, 2013
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